ABSTRACT
Susac syndrome is a rare disease thought to develop secondary to microvascular damage in the brain, inner ear, and retina. Considering that anti-endothelial cell antibodies are involved in its pathogenesis, treatment is largely provided with immunosuppressant drugs. Early initiation of treatment and aggressive therapy have a positive effect on long-term outcomes. Although there is no clear evidence that Susac syndrome creates a predisposition to thrombosis, in our case, the detection of significant coronary artery disease that would require revascularization in a patient diagnosed with Susac syndrome who presented with acute coronary syndrome clinic supports this idea. In this case report, the difficulties in the revascularization process, the decisions made, and other alternative approaches in the patient with Susac syndrome will be reviewed. Our case is the first in the literature to describe the coexistence of Susac syndrome and acute coronary syndrome. More case reports are needed to further elucidate Susac syndrome and its cardiac effects. Keywords: Acute Coronary Syndrome,Susac Syndrome,Coronary Artery Disease
Cite this Article As :
Gurbuz AS, Gur S, Sahin AT, Kesriklioglu S, Yavuz YE. Acute Coronary Syndrome In Patient With Susac Syndrome: A Case Report. Selcuk
Med J 2024;40(4): 199-201
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Case Report
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Keywords
Acute Coronary Syndrome, Susac Syndrome, Coronary Artery Disease
