Interrupted aortic arch

Interrupted aortic arch is defined as a complete separation of ascending and descending aorta. Our patient was classified type B whose interruption was between the left common carotid and subclavian arteries. Type B interrupted aortic arch associated with other extracardiac and intracardiac congenital lesions is a lethal defect. However, interruption of the aotic arch in association with ventricular inversion, hypoplastic left ventricul and double inlet left ventricul is a very rare condition. We report one case whose survival was provided by primary cardiac repair.